What is the pathology in truncus arteriosus?

What is the pathology in truncus arteriosus?

Truncus arteriosus is a birth defect of the heart. It occurs when the blood vessel coming out of the heart in the developing baby fails to separate completely during development, leaving a connection between the aorta and pulmonary artery.

What is Tapvc?

Total anomalous pulmonary venous return (TAPVR) (pronounced TOHT-l uh-NOM-uh-luh-s PUHL-muh-ner-ee VEE-nuh-s ri-TURN), or connection (TAPVC) is a birth defect of the heart in which the veins bringing blood back from the lungs (pulmonary veins) don’t connect to the left atrium like usual.

What is the main branches of truncus arteriosus?

Truncus arteriosus type I is characterized by origin of a single pulmonary trunk from the left lateral aspect of the common trunk, with branching of the left and right pulmonary arteries from the pulmonary trunk.

What is TGA disease?

Transposition of the great arteries, or TGA, is a heart defect that occurs when the two main blood vessels leaving the heart are in abnormal positions. TGA is a life-threatening congenital condition, meaning it is present at birth. Babies with TGA need surgery.

How is Eisenmenger diagnosed?


  1. Blood tests. Blood tests may be done to check your blood cell counts, which are often high in Eisenmenger syndrome.
  2. Electrocardiogram (ECG).
  3. Chest X-ray.
  4. Echocardiogram.
  5. Computerized tomography (CT) scan.
  6. Magnetic resonance imaging (MRI).
  7. Cardiac catheterization.
  8. Walking test.

What is PAPV?

Partial anomalous pulmonary venous return (PAPVR) is a rare heart defect that’s present at birth (congenital heart defect).

What is D-TGA and L-TGA?

L-transposition of the great arteries (L-TGA) is also known as congenitally corrected transposition of the great arteries. This condition is different from D-transposition of the great arteries (d-TGA). In L-TGA, the right and left lower pumping chambers of the heart (ventricles) are switched.

What is Eisenmenger?

Eisenmenger (I-sun-meng-uhr) syndrome is a long-term complication of an unrepaired heart defect that someone was born with (congenital). The congenital heart defects associated with Eisenmenger syndrome cause blood to circulate abnormally in your heart and lungs.

Which radiographic findings are characteristic of truncus arteriosus type I (tar)?

Plain frontal chest radiograph in an infant with truncus arteriosus type I demonstrates moderate cardiomegaly with increased pulmonary arterial circulation (plethoric lung). A large, right-sided aortic arch is noted. Image courtesy of Daniel J Diana, MD, Director of Pediatric Cardiology, University of Connecticut.

Can echocardiography diagnose truncus arteriosus?

Echocardiography is the modality of choice for diagnosing truncus arteriosus. The other investigations noted in this section are complementary. Echocardiography has markedly changed the evaluation, diagnosis, and management of congenital heart disease .

What are the 4 types of truncus arteriosus?

CLASSIFICATIONS. It divides truncus arteriosus into four types, I to IV ( Fig. 45-1 ). In Collett and Edwards type I, a common arterial trunk divides into an aorta and a short pulmonary trunk, which divides into the left and right branch pulmonary arteries. This is the most common configuration (48% to 68% of cases).

Is nuclear medicine useful for the diagnosis of truncus arteriosus?

Echocardiography is an operator-dependent modality, even more so than other cardiovascular techniques. Nuclear medicine studies have limited usefulness in the diagnosis and treatment of truncus arteriosus; at times, however, nuclear medicine comes into play.